Correction of tetralogy of Fallot with absent pulmonary valve syndrome in a young infant using a bicuspid equine pericardial tube

Research output: Contribution to journalArticle

2 Citations (Scopus)

Abstract

Absent pulmonary valve syndrome (APVS) is an uncommon variant of tetralogy of Fallot (TOF), which manifests morphologically as vestigial pulmonary valve cusps at the right ventricle-pulmonary trunk junction. The aneurysmally dilated pulmonary arteries may compress the tracheobronchial tree and cause severe respiratory distress in the neonatal or infant stage. Early surgical correction in these patients is necessary despite the high operative mortality rate. A 1-day-old male neonate suffered from progressive shortness of breath after birth. Echocardiography confirmed the diagnosis of TOF with APVS. The marked dilatation of pulmonary arteries resulted in airway compression in addition to heart failure. Total surgical correction was performed at 40 days of age, using a homemade bicuspid equine pericardial tube for right ventricular outflow reconstruction. The short-term follow-up echocardiogram demonstrated good motility of the pericardial leaflet. However, patients receiving this type of valved conduit require meticulous long-term follow-up.

Original languageEnglish
Pages (from-to)329-333
Number of pages5
JournalJournal of the Formosan Medical Association
Volume105
Issue number4
DOIs
Publication statusPublished - 2006 Apr

All Science Journal Classification (ASJC) codes

  • Medicine(all)

Fingerprint Dive into the research topics of 'Correction of tetralogy of Fallot with absent pulmonary valve syndrome in a young infant using a bicuspid equine pericardial tube'. Together they form a unique fingerprint.

  • Cite this