Crossed fused renal ectopia with segmental fusion of bilateral ureters and abdominal aortic anomalies in a patient with caudal regression syndrome

Y. C. Duh, Shu-Ti Chia, J. C. Sheu, C. C. Peng

Research output: Contribution to journalArticle

Abstract

Caudal regression syndrome consists of multiple congenital anomalies, mainly caudal segment defects. We describe a preterm baby born to a healthy mother with typical caudal regression picture, including imperforated anus with rectovesical fistula, sacral agenesis, multiple rib and vertebral anomalies, and club feet. Crossed fused renal ectopia with fused ureters resulting in urinary obstruction was managed with transureteroureterostomy and cutaneous vesicostomy. We also found a single large umbilical artery with high abdominal aortic insertion which usually presents in sirenomelia. Because of the anatomical diversity of the urinary and cardiovascular systems associated with multiple congenital anomalies, careful evaluation is mandatory.

Original languageEnglish
Pages (from-to)370-372
Number of pages3
JournalEuropean Journal of Pediatric Surgery
Volume17
Issue number5
DOIs
Publication statusPublished - 2007 Oct 1

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Single Umbilical Artery
Cystostomy
Ectromelia
Anal Canal
Ribs
Ureter
Cardiovascular System
Fistula
Foot
Mothers
Kidney
Skin
Fused Kidney
Sacral defect and anterior sacral meningocele

All Science Journal Classification (ASJC) codes

  • Pediatrics, Perinatology, and Child Health
  • Surgery

Cite this

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Crossed fused renal ectopia with segmental fusion of bilateral ureters and abdominal aortic anomalies in a patient with caudal regression syndrome. / Duh, Y. C.; Chia, Shu-Ti; Sheu, J. C.; Peng, C. C.

In: European Journal of Pediatric Surgery, Vol. 17, No. 5, 01.10.2007, p. 370-372.

Research output: Contribution to journalArticle

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