Primary granulomatous angiitis of the central nervous system with amyloid angiopathy

A case report and literature review

Research output: Contribution to journalArticle

3 Citations (Scopus)

Abstract

Primary angiitis of the central nervous system is a rare idiopathic inflammation of vessels. We report on a 75-year-old male with primary angiitis of the central nervous system and cerebral amyloid angiopathy. He presented with subacute onset of progressive decline in cognitive functions, followed by confusion and coma. Initial brain magnetic resonance imaging favored meningoencephalitis. There was no improvement after treatment with antibiotics. Final diagnosis was proven by brain biopsy. Corticosteroids were given, but without significant improvement. This case is reported because of its rarity and its clinical presentation.

Original languageEnglish
Pages (from-to)73-78
Number of pages6
JournalNeurologist
Volume19
Issue number3
DOIs
Publication statusPublished - 2015 Feb 1

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Cerebral Amyloid Angiopathy
Confusion
Meningoencephalitis
Brain
Coma
Cognition
Adrenal Cortex Hormones
Magnetic Resonance Imaging
Anti-Bacterial Agents
Inflammation
Biopsy
Primary angiitis of the central nervous system
Granulomatous Angiitis of the Central Nervous System
Amyloid angiopathy

All Science Journal Classification (ASJC) codes

  • Clinical Neurology

Cite this

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AB - Primary angiitis of the central nervous system is a rare idiopathic inflammation of vessels. We report on a 75-year-old male with primary angiitis of the central nervous system and cerebral amyloid angiopathy. He presented with subacute onset of progressive decline in cognitive functions, followed by confusion and coma. Initial brain magnetic resonance imaging favored meningoencephalitis. There was no improvement after treatment with antibiotics. Final diagnosis was proven by brain biopsy. Corticosteroids were given, but without significant improvement. This case is reported because of its rarity and its clinical presentation.

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